Cystic Fibrosis (CF) is a rare, inherited disease that primarily affects the lungs and digestive system. It is caused by mutations in the CFTR gene, leading to thick and sticky mucus in the airways. This mucus impairs normal airway clearance, increases susceptibility to infections, and causes progressive lung disease.
Advances in treatment have significantly improved survival and quality of life for people with CF. However, respiratory complications remain the main cause of illness and long-term health burden, making ongoing research into lung function, airway disease, and novel therapies essential.
At CPlung, we focus on understanding and improving respiratory outcomes in children with cystic fibrosis through clinical research, advanced lung function testing, imaging, and translational studies.
AKTIVE STUDIER
Pancreas
Kadence
Vertex
Ansvarlige
Navn
Billede
Copenhagen Paediatric Lung Lab 